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日本呼吸器学会英文誌 Respiratory Investigation
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Abstract

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Article in Japanese

Case Report

A case of lymphangioleiomyomatosis with atypical radiological features and slow progression

Midori Sugisakia,*  Tatsuji Enomotoa,#  Tetsuya Yokosukab  Takuo Hayashic  Ryota Ushioa,†  Toshiko Kobayashib  Shinji Abea 

aDepartment of Respiratory Medicine, Tokyo Metropolitan Hiroo Hospital
bDepartment of Surgery, Tokyo Metropolitan Hiroo Hospital
cDepartment of Human Pathology, Juntendo University School of Medicine
*Present address: Department of Respiratory Medicine, Kanagawa Cardiovascular and Respiratory Center
#Present address: Department of Respiratory Medicine, Ofuna Chuo Hospital
Present address: Department of Respiratory Medicine, Yokohama City University Hospital

ABSTRACT

A 37-year-old female was admitted because of recurrent pneumothorax. Chest CT showed right pneumothorax and 5 thin-wall cysts 2.0-3.5 cm in diameter. These findings had been almost stable for one year. A histopathological examination revealed typical findings of lymphangioleiomyomatosis (LAM) with an atypical area that showed a few lymphatic vessels and prominent capillaries and was also negative for α-SMA and VEGF-D. This case is thought to be a rare LAM lacking in lymphangiogenesis.

KEYWORDS

Lymphangioleiomyomatosis  Pneumothorax  Lung cyst  Lymphangiogenesis 

Received 6 Aug 2013 / Accepted 18 Nov 2013

AJRS, 3(2): 251-254, 2014

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