A 77-year-old woman had been receiving regular outpatient treatment for primary thymic mucosa-associated lymphoid tissue lymphoma, pulmonary amyloidosis, and Sjögren's syndrome. In 20XX－4, the patient was referred to the Department of Respiratory Medicine with a diagnosis of pulmonary Mycobacterium avium complex infection. Treatment with rifampicin, ethambutol, and clarithromycin was initiated but because of the development of adverse events, such as hearing loss, she was subsequently kept on watchful waiting. In July 20XX, she presented with hemoptysis. As a result, she was intubated and ventilated. Bronchial artery embolization was performed, and the hemoptysis improved. However, ventilator-associated pneumonia developed, and she subsequently died on hospital day 12. After receiving consent from her family, an autopsy was performed. We report our experience of a rare case, in which various pulmonary lesions had been observed on imaging examinations over a period of 11 years and review the associated literature.