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Vol.38 No.6 contents Japanese/English

- Case Report -

Two Cases of Malignant Mediastinal Schwannoma with von Recklinghausen's Disease

Mitsuo Kawamura, Ichirou Suzuki, Kimito Orino and Yoshirou Sazawa
Department of Chest Surgery, Nakadohri General Hospital

We report two cases of malignant mediastinal schwannoma with von Recklinghausen's disease. A 16-year-old girl (case 1) was admitted with right chest pain due to right pleural effusion. Her chest X-ray after aspiration of the effusion showed a giant cystic tumor in the posterior mediastinum. Tumor extirpation failed because of marked bleeding and only biopsy was performed. The histological diagnosis was malignant schwannoma. She died 3 mounths after the biopsy. A 39-year-old woman (case 2) was admitted with dyspnea. Her chest X-ray showed a large tumor shadow in the right upper lung field. Tumor extirpation was performed using the partial cardiopulmonary bypass. In spite of reoperation for postoperative bleeding, she recovered and was discharged. Histological examination disclosed malignant schwannoma with rhabdomyosarcoma (malignant triton tumor). The tumor recurred at the left adrenal gland, but was totally removed through laparotomy. She is alive 29 monthes after the initial operation. In patients with von Recklinghausen's disease, careful attention to the malignant mediastinal neurogenic tumor is necessary.
key words: Mediastinal tumor, Malignant schwannoma, Malignant triton tumor, Von Recklinghausen's disease

Received: July 9, 1998
Accepted: August 10, 1998

JJLC 38 (6): 715-720, 1998

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