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The Japanese journal of neuropsychology
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Full Text of this Article
in Japanese PDF (970K)
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ArticleTitle
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Neuropsychological findings of frontotemporal dementia with motor neuron disease |
Language |
J |
AuthorList |
Yoshio Mitsuyama |
Affiliation |
Division of Gerontopsychiatry, Daigo Hospital |
Publication |
Japanese Journal of Neuropsychology: 28 (3), 199-206, 2012 |
Received |
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Accepted |
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Abstract |
The clinico-pathological findings of frontotemporal dementia with motor neuron disease (FTD-MND) are reviewed. The characteristic featurres includes:(1) Progressive frontotemporal dementia with slowly progressive onset in the presenile period. Characteristic neuropsychological findings are personality change, emotional disorders and loss of spontaneous speech, global intellectual impairment including memory difficulty. (2) Neurogenic muscular wasting during the course of illness, such as spinal progressive muscular atrophy. (3) A duration of illness to death of from tow to five years. (4) Degenerative changes throughout the CNS shows primary degenerative dementia and motor neuron disease. FTD-MND is a clinico-pathological entity by motor neuron degeneration and the clinical signs of dementia and motor neuron disease. The author has reporetd the possibility of a new disease entity. |
Keywords |
frontotemporal dementia, motor neuron disease |
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